Choledochal cysts are focal dilations of the extra and/or intrahepatic bile ducts without mechanical distal obstruction. The cause is debatable ranging from intrauterine infections to abnormal reflux of pancreatic juices into the choledochus. A majority present by the first decade of life. The problem is functional obstruction to the flow of bile leading to stasis, stone formation, infection and pancreatitis. In a minority of cases the symptoms are vague and often mild in nature leading to misdiagnosis until adulthood. The prolonged biliary stasis can lead to persistent hepatocyte damage and eventually fibrosis and even cirrhosis. More importantly perisistent inflammation can result in metaplasia, dysplasia and carcinogenesis within the biliary tract. In fact more than half adults operated for choledochal cysts may contain malignancy. I recently operated a 55 year old man with jaundice and liver fibrosis who had abdominal symptoms for 15 years but never investgated until he developed jaundice. Fortunately there was no malignancy in the specimen.

Operation for choledochal cyst in an adult with jaundice and liver fibrosis




